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Perianal rhabdomyosarcoma in an adult: A case report and review of the literature

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收录情况: ◇ SCIE

机构: [1]Hebei Med Univ, Affiliated Hosp 1, Dept Gen Surg, Shijiazhuang, Peoples R China [2]Hebei Med Univ, Affiliated Hosp 4, Dept Endocrinol, Shijiazhuang, Peoples R China [3]Hebei Med Univ, Affiliated Hosp 4, Dept Pathol, Shijiazhuang, Peoples R China [4]Hebei Med Univ, Affiliated Hosp 4, Dept Gen Surg, Shijiazhuang, Peoples R China [5]Hebei Med Univ, Affiliated Hosp 4, Dept Gen Surg, 12 Jiankang Rd, Shijiazhuang 050011, Peoples R China
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关键词: operation perianal/perineal rhabdomyosarcomas surgery treatment

摘要:
Perianal/perineal rhabdomyosarcomas (PRMS) is rare, and the outcome is poor. A 29-year-old female presented with perineal rhabdomyosarcomas revealed metastases to inguinal lymph nodes on the bilateral side. Disease progression was discovered when the patient got adjuvant epirubicin, ifosfamide, and bevacizumab for 2 cycles. After 3 cycles of nivolumab, dacarbazine, cisplatin, and vinblastine therapy, a partial response was identified in the patient. The surgical resection was performed. The patient received neoadjuvant chemotherapy before surgery and was weak after surgery, so he did not receive chemoradiotherapy. The patient succumbed after 11 months postoperatively due to widespread intraabdominal metastasis.

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出版当年[2023]版:
大类 | 4 区 医学
小类 | 4 区 医学:内科
最新[2025]版:
大类 | 4 区 医学
小类 | 4 区 医学:内科
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出版当年[2023]版:
Q2 MEDICINE, GENERAL & INTERNAL
最新[2024]版:
Q2 MEDICINE, GENERAL & INTERNAL

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第一作者机构: [1]Hebei Med Univ, Affiliated Hosp 1, Dept Gen Surg, Shijiazhuang, Peoples R China
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通讯机构: [4]Hebei Med Univ, Affiliated Hosp 4, Dept Gen Surg, Shijiazhuang, Peoples R China [5]Hebei Med Univ, Affiliated Hosp 4, Dept Gen Surg, 12 Jiankang Rd, Shijiazhuang 050011, Peoples R China
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